Connective tissue disease (CTD), Pulmonary arterial hypertension (PAH), HFA-PEFF score, All-cause mortality, Clinical worsening events, Diseases of the circulatory (Cardiovascular) system, RC666-701

Abstract Background Connective tissue disease-associated pulmonary arterial hypertension (CTD-PAH) patients with left heart dysfunction may have worse prognosis. This study was to investigate the prognostic value of HFA-PEFF score in connective tissue disease-associated PAH. Methods This single-center retrospective cohort study enrolled 147 CTD-PAH patients diagnosed via right heart catheterization (RHC), divided into two groups based on their HFA-PEFF scores: