синдром майера-рокитанского-кюстнера-хаузера, аплазия влагалища, матки, Pediatrics, RJ1-570, Gynecology and obstetrics, RG1-991

The Mayer-Rokitansky-Custer-Hauser syndrome (SMRCX) is a violation of the intrauterine development of the Pmuller ducts, leading to aplasia of the vagina and uterus. It is diagnosed in 1 out of 4500-5000 newborn girls. The etiology of the syndrome has not been sufficiently studied. According to world statistics, the role of hereditary factors in the formation of malformations of the reproductive system ranges from 10 to 25 %. This article describes a rare clinical case of MRC syndrome. Considering the optimal chosen management tactics of the patient, a favorable outcome was obtained for the woman.